Nuss Procedure and Factor VII Deficiency: A Case Report
Nesimi Günal
Department of Thoracic Surgery, Kairikkale University, School of Medicine, Kairikkale, Turkey.
Ayse Anil Karabulut
Department of Dermatology, Kairikkale University, School of Medicine, Kairikkale, Turkey.
Meryem Albayrak
Department of Pediatric Hematology, Kairikkale University, School of Medicine, Kairikkale, Turkey.
Koray Dural
Department of Thoracic Surgery, Kairikkale University, School of Medicine, Kairikkale, Turkey.
Berkant Özpolat *
Department of Thoracic Surgery, Kairikkale University, School of Medicine, Kairikkale, Turkey.
*Author to whom correspondence should be addressed.
Abstract
A 19 year-old boy admitted with pain and discoloration on his chest wall 18 months after a Nuss procedure performed for pectus excavatum deformity. His physical examination revealed that this skin lesion was an ecchymosis. We diagnosed a very rare bleeding disorder due to Factor VII deficiency which is a recessively inherited coagulation disorder where even spontaneous bleedings may be seen. We aimed to discuss the management of the patient, if it had been diagnosed preoperatively and the preoperative preparation before the bar removal.
Keywords: Pectus excavatum, factor vii, ecchymosis, internal normalized ratio.