Anomalous Orıgın of the Left Pulmonary Artery from the Ascendıng Aorta wıth Pulmonary Atresıa ın a 13 Year-old Girl
Tuba Selcuk *
Department of Radiology, Istanbul Haseki Education and Research Hospital, Haseki, Istanbul, Turkey and Department of Medical Sciences, Gelisim University, Avcılar, Istanbul, Turkey.
Cigdem Bilgili
Department of Radiology, Istanbul Haseki Education and Research Hospital, Haseki, Istanbul, Turkey.
Hafize Otcu
Department of Radiology, Reyhanlı Government Hospital, Reyhanlı, Hatay, Turkey.
Yildiray Savas
Department of Radiology, Istanbul Haseki Education and Research Hospital, Haseki, Istanbul, Turkey.
Gulfidan Cakmak
Department of Pulmonary Medicine, Istanbul Haseki Education and Research Hospital, Haseki, Istanbul, Turkey.
Ferhat Cengel
Department of Radiology, Istanbul Haseki Education and Research Hospital, Haseki, Istanbul, Turkey.
*Author to whom correspondence should be addressed.
Abstract
Aim: We reported a rare case of an anomalous origin of the left pulmonary artery (AOLPA) from the ascending aorta associated with pulmonary atresia and right sided aortic arch diagnosed at a relatively late age.
Case: 13 year-old girl presented to our pulmonology clinic with complaints of cough and dyspnea. On chest X-ray cardio thoracic ratio was increased and shadow of the arch was not seen on the left. On her echocardiography pulmonary arteries couldn't be demonstrated. Computed tomography angiography was performed to the patient. Right sided arch aorta with pulmonary atresia associated with an anomalous origin of the left pulmonary artery from the ascending aorta with a well developed collateral blood supply to the right lung and coexisting pulmonary infection was detected. She was managed medically. She is on the first year of her follow up. Her medical status is stable.
Conclusion: We presented a case of relatively rarely seen anomalous origin of the left pulmonary artery from the ascending aorta with a rarely seen association of pulmonary atresia and wanted to take attention to its presentation in a late childhood.
Keywords: Pulmonary atresia, anomalous origin, right sided aortic arch