Cystic Partially Differentiated Nephroblastoma, A Hyperfavourable Variant of Nephroblatoma: A Case Report with Review of the Literature
B. A. Ojo *
Department of Histopathology, College of Health Sciences, Benue State University, Makurdi, Nigeria.
W. T. Yongo
Department of Surgery, College of Health Sciences, Benue State University, Makurdi, Nigeria.
C. T. Soo
Department of Surgery, College of Health Sciences, Benue State University, Makurdi, Nigeria.
I. T. Annongu
Department of Radiology, College of Health Sciences, Benue State University, Makurdi, Nigeria.
R. Vhriterhire
Department of Histopathology, College of Health Sciences, Benue State University, Makurdi, Nigeria.
H. Mohammed
Department of Radiology, College of Health Sciences, Benue State University, Makurdi, Nigeria.
E. I. Ogwuche
Department of Surgery, College of Health Sciences, Benue State University, Makurdi, Nigeria.
O. Shorun
Department of Histopathology, Benue State University Teaching Hospital, Makurdi, Nigeria.
I. V. Ugwu
Department of Anatomic Pathology, National Orthopedic Hospital, Enugu, Nigeria.
E. O. Umobong
Histoconsult Laboratories, Garki, Abuja, Nigeria.
B. Eke
Department of Surgery, College of Health Sciences, Benue State University, Makurdi, Nigeria.
D. J. Omeh
Department of Surgery, Benue State University Teaching Hospital, Makurdi, Nigeria.
M. O. Ogiator
Department of Medicine, College of Health Sciences, Benue State University, Makurdi, Nigeria.
P. Abayol
College of Health Sciences, Benue State University, Makurdi, Nigeria.
*Author to whom correspondence should be addressed.
Abstract
Cystic partially differentiated nephroblastoma is a rare variant of Wilm’s tumor and it represents the hyperfavourable end of the Wilm’s spectrum affecting young children.
We described the first documented case from the northern part of Nigeria. The index patient presented with left flank mass. He had unilateral nephrectomy and surgical pathology established its diagnosis.
It is a lower risk but malignant tumor that comes as the differential diagnosis of pediatric cystic renal lesions and need to be differentiated from benign lesions such as cystic nephroma and mixed epithelial and stroma tumor of kidney. It should always be considered as a differential diagnosis of childhood abdominal mass with appropriate investigations and management since it is curable by nephrectomy alone.
Keywords: Cystic partially differentiated nephroblastoma, Wilm’s tumor, cystic nephroma